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MRKH Center | Mayer-Rokitansky-Küster-Hauser Syndrome

<p>MRKH Center | Mayer-Rokitansky-Küster-Hauser Syndrome</p>

Offering Care and Support for Mayer-Rokitansky-Küster-Hauser (MRKH) Syndrome

About 1 in 5,000 girls will be born with MRKH syndrome, although they’re typically diagnosed in adolescence. Young women diagnosed with MRKH face a spectrum of concerns from the time of diagnosis through their reproductive years, including a higher risk of associated conditions, such as endometriosis and anomalies of the urinary tract and spine. A smaller percentage of women may have underdeveloped uterine remnants, which can cause pelvic pain. While women with MRKH have normal female genetics, given the lack of uterus or variation in the development of the uterus and vagina, periods will not occur.

Through our center, you’ll have access to world-renowned specialists in pediatric and adolescent gynecology, pediatric genetics, reproductive genetics, psychology, reproductive endocrine and infertility, maternal fetal medicine, minimally invasive gynecology, radiology and transplant surgery — all under one roof.

Treatments offered at the MRKH Center

Recommended treatment options will depend on your specific anatomy, life stage and goals for building a family. No other center offers the full breadth of treatment options we’re able to offer through Texas Children’s Hospital and the Pavilion for Women at Texas Children’s. Specific options may include:

  • Uterine remnant management: Some women may require endometriosis care to control pelvic pain symptoms.
  • Vaginal dilation: MRKH is associated with a shortened vagina, and vaginal dilators are one treatment option to help stretch the vagina.
  • Vaginoplasty: Vaginoplasty is a surgical procedure to create a vagina. We offer both minimally invasive and robotic surgery options for children and adolescents.
  • Family fertility options: As women become interested in building a family, egg harvesting with surrogacy and uterine transplant are available through our Family Fertility Center and Uterus Transplant Research Program. 

 

Related Departments